S Eriksson, I Hägerstrand - Acta Med Scand, 1974 - interscience.wiley.com Abstract. Clinical and laboratory findings in 9 adults with homozygous (Pi zz )
α 1 -antitrypsin (AAT) deficiency and cirrhosis of the liver are described.
This clinical entity is characterized by rapidly progressive cirrhosis in ... Cited by 91 - Related articles - All 2 versions
DR Triger, GH Millward-Sadler, AA … - QJM, 1976 - Oxford Univ Press SUMMARY Thirteen adult patients (aged 16 to 73 years) from 12 families are
described -with liver disease and alpha-1-antitrypsin deficiency. Long-term
observation of several of these patients suggests that the liver disease ... Cited by 32 - Related articles
EJ Wilkinson, K Raab, CA Browning, TA Hosty - The Journal of Pediatrics, 1974 - Elsevier August 1974 The Journal of PEDIATRICS 1 5 9 Familial hepatic cirrhosis in
infants associated with alpha,-antitrypsin SZ phenotype Two sibling neonates are
described, each of whom died within the first two weeks Qf l~fe. Each had ... Cited by 18 - Related articles - All 4 versions
CH Chan, CJ Steer, J Vergalla, EA Jones - The American Journal of Medicine, 1978 - Elsevier Following the incidental finding of hepatomegaly in a 39 year old white man from
the Dominican Republic, a liver biopsy disclosed chronic active hepatitis and
cirrhosis. Six years later, after presenting with upper abdominal pains due ... Cited by 14 - Related articles - All 2 versions
F Brandrup, PA Ostergaard - Archives of Dermatology, 1978 - archderm.highwire.org \s=b\\g=a\1-Antitrypsin (\g=a\1-AT) deficiency is an autosomal recessive
inherited disease. The serum concentration of the protease inhibitor (Pi)
\g=a\1-AT is controlled by a set of codominant allelic genes, constituting ... Cited by 13 - Related articles - All 3 versions
AJ Greenwald, DS Johnson, RM Oskvig, CA … - JAMA: the journal of the American Medical Association, 1975 - ncbi.nlm.nih.gov An elderly man with long-standing pulmonary emphysema was seen with recent onset
of steatorrhea and ascites. He had very low levels of serum alpha1-antitrypsin,
hepatic cirrhosis, and intestinal mucosal atrophy. We believe this this ... Cited by 12 - Related articles - All 2 versions
- ►nih.gov [PDF] PW Brunt - British Medical Journal - gut.bmj.com Page 1. doi:10.1136/gut.15.7.573 1974;15;573-580 Gut PW Brunt Antitrypsin and the
liver. http://gut.bmj.com Updated information and services can be found at: ... Cited by 8 - Related articles - All 4 versions
HA Campana, YS Park, GD Gourgoutis - Digestive Diseases and Sciences, 1974 - Springer Congenital hepatic fibrosis (CHF) was detected in a 10,year-old boy with
hepatosplenomegaly and leukopenia and in a 45-year-old man with hepatomegaly.
Several years after these original findings, both patients developed ... Cited by 4 - Related articles - All 2 versions
