A AGOSTONI, M CICARDI - Medicine, 1992 - journals.lww.com HEREDITARY AND ACQUIRED CI INHIBITOR DEFICIENCY 207 Diagnostic criteria Diagnosis
of HAE was based on a personal and/or family history of recurrent non-inflammatory subcutaneous
edema, episodic abdominal pain, and laryngeal edema in patients with functional Cl-INH ... Cited by 232 - Related articles - All 3 versions
AT Waytes, FS Rosen, MM Frank - The New England journal of …, 1996 - nejm.highwire.org Methods We conducted two double-blind, placebo-controlled studies. The first was a crossover
study consisting of two 17-day trials in which prophylactic infusions of either C1 inhibitor (25
plasma units per kilogram of body weight) or placebo were given intravenously every ... Cited by 175 - Related articles - BL Direct - All 5 versions
K Bork, SE Barnstedt, P Koch, H Traupe - The Lancet, 2000 - Elsevier 94 HAE cases with C1-inhibitor deficiency, positive family history, or both were identified. Biochemical
testing showed that 84 patients from 49 families had a functional C1-inhibitor deficiency. 11 of
these patients had no affected family members (probably representing de-novo ... Cited by 141 - Related articles - BL Direct - All 7 versions
A Agostoni, E Aygören-Pürsün, KE Binkley, A … - The Journal of Allergy and …, 2004 - Elsevier Hereditary angioedema (HAE), a rare but life-threatening condition, manifests as acute attacks
of facial, laryngeal, genital, or peripheral swelling or abdominal pain secondary to intra-abdominal
edema. Resulting from mutations affecting C1 esterase inhibitor (C1-INH), inhibitor of the ... Cited by 124 - Related articles - All 3 versions
- ►pnas.org [PDF] D Stoppa-Lyonnet, PE Carter, T Meo, … - Proceedings of the …, 1990 - National Acad Sciences Page 1. Proc. Natl. Acad. Sci. USA Vol. 87, pp. 1551-1555, February 1990 Genetics Clusters
of intragenic Alu repeats predispose the human C1 inhibitor locus to deleterious rearrangements
(genetic disease/hereditary angioedema/serine protease inhibitor/complement) ... Cited by 123 - Related articles - All 8 versions
UC Nzeako, E Frigas, WJ Tremaine - Archives of Internal Medicine, 2001 - archinte.highwire.org Hereditary angioedema (HAE) is an autosomal dominant disease that afflicts 1 in 10 000 to 1
in 150 000 persons; HAE has been reported in all races, and no sex predominance has been
found. It manifests as recurrent attacks of intense, massive, localized edema without ... Cited by 117 - Related articles - BL Direct - All 4 versions
W Vleeming, JGC Van Amsterdam, BHC Stricker, DJ … - Drug Safety, 1998 - ingentaconnect.com Summary Available information from 1980 to 1997 on angiotensin converting enzyme (ACE)
inhibitor–induced angioedema and its underlying mechanisms are summarised and
discussed. The incidence of angioedema is low (0.1 to 0.2%) but can be considered as a ... Cited by 119 - Related articles - BL Direct - All 5 versions
MM Gompels, RJ Lock, M Abinun, CA … - Clinical and …, 2005 - pubmedcentral.nih.gov We present a consensus document on the diagnosis and management of C1 inhibitor
deficiency, a syndrome characterized clinically by recurrent episodes of angio-oedema. In hereditary
angio-oedema, a rare autosomal dominant condition, C1 inhibitor function is reduced due ... Cited by 104 - Related articles - BL Direct - All 5 versions
FH Messerli, J Nussberger - The Lancet, 2000 - Elsevier Elsewhere in today's Lancet, Jean Rouleau and colleagues report a comparison of omapatrilat
with lisinopril in 573 patients with class II to IV congestive heart failure (CHF). The investigators
found no difference between the two drug classes in the primary endpoint (exercise ... Cited by 109 - Related articles - BL Direct - All 2 versions
