H GRIERSON, DT PURTILO - Annals of internal medicine, 1987 - Am Coll Physicians A registry of persons with the X-linked lymphoproliferative syndrome, which is
characterized by marked susceptibility to diseases induced by the Epstein-Barr
virus, has enrolled 161 patients within 44 kindreds. Fifty-seven percent of ... Cited by 115 - Related articles - All 4 versions
DS Harrington, DD Weisenburger, DT Purtilo - Cancer, 1987 - be-md.ncbi.nlm.nih.gov Male patients with the X-linked lymphoproliferative syndrome (XLP) have an
inherited immune deficiency to Epstein-Barr virus (EBV) infection that results
in fatal infectious mononucleosis (IM), acquired hypogammaglobulinemia- or ... Cited by 79 - Related articles - All 3 versions
JC Skare, A Milunsky, KS Byron, JL Sullivan - Proc Natl Acad Sci USA, 1987 - National Acad Sciences Proc. Natl. Acad. Sci. USA Vol. 84, pp. 2015-2018, April 1987 Medical Sciences ... (immunodeficiency/Epstein-Barr virus/restriction fragment length
polymorphism) ... JAMES C. SKARE*, AUBREY MILUNSKY*, KEVIN S. BYRONt, AND ... Cited by 54 - Related articles - All 10 versions
JC Skare, HL Grierson, JL Sullivan, RL … - Human genetics, 1989 - Springer 1 Center for Human Genetics and Departments of Pediatrics and Microbiology,
Boston University School of Medicine, Boston, MA 02118, USA 2Department of
Pathology and Microbiology, University of Nebraska Medical Center, Omaha, ... Cited by 42 - Related articles - All 3 versions
DT Purtilo, HL Grierson, H Ochs, J Skare - The American Journal of Medicine, 1989 - Elsevier : Concordance for detection of affected males was 100% when linkage analysis
using DXS42 and DXS37 DNA probes and antibody responses to challenge with
bacteriophage ΦX174 were both determined. Most affected males showing IgG ... Cited by 31 - Related articles - All 7 versions
HL Grierson, J Skare, J Hawk, M Pauza, DT … - Am J Med Genet, 1991 - interscience.wiley.com Patients with X-linked lymphoproliferative (XLP) disease are characterized by
extreme vulnerability to Epstein-Barr virus (EBV). Following infection with EBV,
affected males develop fatal infectious mononucleosis (IM), ... Cited by 49 - Related articles - All 3 versions
DT Purtilo, HL Grierson - Cancer genetics and cytogenetics, 1991 - Elsevier During the past decade, 240 males with X-linked lymphoproliferative disease
(XLP) within 59 unrelated kindreds have been identified worldwide. One half of
the patients have developed fatal infectious mononucleosis, about one third ... Cited by 39 - Related articles - All 3 versions
DT Purtilo, JP Yang… - The Lancet, 1975 - Elsevier Of 18 boys in the Duncan kindred, 6 died of a lymphoproliferative disease. They
exhibited a subtle, progressive combined variable immunodeficiency disease
characterised by benign or malignant proliferation of lymphocytes, ... Cited by 314 - Related articles - All 5 versions
EC Mroczek, DD Weisenburger, HL Grierson, R … - Archives of pathology & laboratory medicine, 1987 - ncbi.nlm.nih.gov A detailed clinicopathologic analysis of 52 cases of fatal infectious
mononucleosis was performed. Fever, rash, generalized lymphadenopathy,
hepatosplenomegaly, and blood cytopenias were the characteristic findings. ... Cited by 99 - Related articles - All 2 versions
DT Purtilo, K Sakamoto, V Barnabei, J Seeley, … - The American Journal of Medicine, 1982 - Elsevier Analyses of 100 subjects with the X-linked lymphoproliferative syndrome (XLP) in
25 kindreds revealed four major interrelated phenotypes: infectious
mononucleosis, malignant B-cell lymphoma, aplastic anemia, and ... Cited by 112 - Related articles - All 2 versions
