Authors
Isabelle Koné-Paut, Fahrad Shahram, Martha Darce-Bello, Luca Cantarini, Rolando Cimaz, Marco Gattorno, Jordi Anton, Michael Hofer, Bouchra Chkirate, Kenza Bouayed, Ilknur Tugal-Tutkun, Jasmin Kuemmerle-Deschner, Hélène Agostini, Sylvia Federici, Armelle Arnoux, Celine Piedvache, Seza Ozen
Publication date
2016/6/1
Journal
Annals of the rheumatic diseases
Volume
75
Issue
6
Pages
958-964
Publisher
BMJ Publishing Group Ltd
Description
Background
We aimed to describe the main features of Behçet's disease (BD) in children in the largest prospective cohort to date and to propose a classification.
Methods
An international expert consensus group was formed to define a data set of minimal symptoms for the inclusion of patients. Patients were entered prospectively during 66 months. Experts classified patients on a consensus basis. The concordance of two international classifications was analysed in confirmed patients with BD. Comparisons of subgroups of patients helped define consensus criteria. BD-associated clinical manifestations were also investigated in three control diseases extracted from an independent data set (Eurofever).
Findings
In total, 42 centres from 12 countries included 230 patients; data for 219 (M/F ratio=1) could be analysed. The experts classified 156 patients (71.2%) as having confirmed BD. Males more often than females …
Total citations
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