Authors
I Koné-Paut, M Darce Bello, F Shahram, M Gattorno, R Cimaz, B Chkirate, K Bouayed, M Hofer, Seza Ozen, J Anton, I Tugal Tutkum, J Kümmerle-Deschner, S Benamour, S Assad Khalil, L Cantarini, A Faye, A Letierce, TA Tran, PedBD group, F Davatchi, O Kasapcopur, A Al Mayouf, C Pajot, S Nielsen, L Lepore, W Bono
Publication date
2011/12
Journal
Pediatric Rheumatology
Volume
9
Pages
1-1
Publisher
BioMed Central
Description
Background
Behçet Disease (BD) is exceptionally observed in children and raises diagnosis problems because there is no specific biologic marker. Sets of clinical criteria have been proposed for adult patients only.
Aim
Is to set-up an international cohort of patients suspected with BD and selected on homogenous criteria. The cohort is aimed at defining an algorithm for definition of the disease in children, reflecting the natural history.
Methods
Centers specializing in PedBD have been called to collaborate documenting their patients into a single online database. An international expert committee has defined inclusion criteria as follows: first sign before 16 years, new patient or patient followed since less than 3 years, patient followed 4 years, consent obtained, and recurrent oral aphthosis [OA](more than 3 attacks/year) associated to at least one of following symptoms: genital ulceration, erythema, folliculitis, pustulous …
Total citations
20181
Scholar articles
I Koné-Paut, MD Bello, F Shahram, M Gattorno… - Pediatric Rheumatology, 2011