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PAULA FERNANDEZ GUERRA
PAULA FERNANDEZ GUERRA
KMEB, Molecular Endocrinology Institute of Clinical Research, University of Southern Denmark
Verified email at health.sdu.dk
Title
Cited by
Cited by
Year
Secondary coenzyme Q10 deficiency and oxidative stress in cultured fibroblasts from patients with riboflavin responsive multiple Acyl-CoA dehydrogenation deficiency
N Cornelius, C Byron, I Hargreaves, P Fernandez Guerra, AK Furdek, ...
Human molecular genetics 22 (19), 3819-3827, 2013
702013
Disease-Associated Mutations in the HSPD1 Gene Encoding the Large Subunit of the Mitochondrial HSP60/HSP10 Chaperonin Complex
P Bross, P Fernandez-Guerra
Frontiers in molecular biosciences 3, 49, 2016
562016
Effects of a Mutation in the HSPE1 Gene Encoding the Mitochondrial Co-chaperonin HSP10 and Its Potential Association with a Neurological and Developmental …
AS Bie, P Fernandez-Guerra, RID Birkler, S Nisemblat, D Pelnena, X Lu, ...
Frontiers in molecular biosciences 3, 65, 2016
512016
Metformin Targets Brown Adipose Tissue in vivo and Reduces Oxygen Consumption in vitro
JN Breining P, Jensen JB, Sundelin EI, Gormsen LC, Jakobsen S, Busk M ...
Diabetes Obesity and Metabolism, 2018
462018
APD-containing cyclolipodepsipeptides target mitochondrial function in hypoxic cancer cells
KM Jacobsen, NL Villadsen, T Tørring, CB Nielsen, T Salomon, ...
Cell Chemical Biology 25 (11), 1337-1349. e12, 2018
272018
Mitochondrial spare respiratory capacity is negatively correlated with nuclear reprogramming efficiency
Y Zhou, RA Al-Saaidi, P Fernandez-Guerra, KK Freude, RKJ Olsen, ...
Stem cells and development 26 (3), 166-176, 2017
252017
Deficiency of the mitochondrial sulfide regulator ETHE1 disturbs cell growth, glutathione level and causes proteome alterations outside mitochondria
N Sahebekhtiari, P Fernandez-Guerra, Z Nochi, J Carlsen, P Bross, ...
Biochimica et Biophysica Acta (BBA)-Molecular Basis of Disease 1865 (1), 126-135, 2019
172019
Functional characterization of the novel intronic nucleotide change c.288+9C>T within the BCKDHA gene: understanding a variant presentation of maple syrup …
P Fernández‐Guerra, R Navarrete, K Weisiger, LR Desviat, S Packman, ...
Journal of Inherited Metabolic Disease: Official Journal of the Society for …, 2010
152010
Bioenergetic and proteomic profiling of immune cells in myalgic encephalomyelitis/chronic fatigue syndrome patients: an exploratory study
P Fernandez-Guerra, AC Gonzalez-Ebsen, SE Boonen, J Courraud, ...
Biomolecules 11 (7), 961, 2021
132021
Selected reaction monitoring as an effective method for reliable quantification of disease‐associated proteins in maple syrup urine disease
P Fernández‐Guerra, RID Birkler, B Merinero, M Ugarte, N Gregersen, ...
Molecular Genetics & Genomic Medicine 2 (5), 383-392, 2014
122014
A cell model for HSP60 deficiencies: modeling different levels of chaperonopathies leading to oxidative stress and mitochondrial dysfunction
C Cömert, P Fernandez-Guerra, P Bross
Protein Misfolding Diseases: Methods and Protocols, 225-239, 2019
112019
Application of an image cytometry protocol for cellular and mitochondrial phenotyping on fibroblasts from patients with inherited disorders
P Fernandez-Guerra, M Lund, TJ Corydon, N Cornelius, N Gregersen, ...
JIMD Reports, Volume 27, 17-26, 2016
82016
GIP reduces osteoclast activity and improves osteoblast survival in primary human bone cells
MS Hansen, K Søe, LL Christensen, P Fernandez-Guerra, NW Hansen, ...
European Journal of Endocrinology 188 (1), 144-157, 2023
52023
A recurrent de novo HSPD1 variant is associated with hypomyelinating leukodystrophy
C Cömert, L Brick, D Ang, J Palmfeldt, BF Meaney, M Kozenko, ...
Molecular Case Studies 6 (3), a004879, 2020
52020
Myalgic encephalomyelitis or chronic fatigue syndrome
L Brinth, H Nielsen, K Varming, SE Boonen, ACG Ebsen, ...
Ugeskrift for laeger 181 (24), V08180570-V08180570, 2019
52019
The psychiatric risk gene BRD1 modulates mitochondrial bioenergetics by transcriptional regulation
V Paternoster, C Cömert, LS Kirk, SH la Cour, T Fryland, ...
Translational Psychiatry 12 (1), 319, 2022
32022
Increased antioxidant response in medium-chain acyl-CoA dehydrogenase deficiency: does lipoic acid have a protective role?
Z Nochi, RID Birkler, P Fernandez-Guerra, J Hansen, F Wibrand, ...
Pediatric Research 88 (4), 556-564, 2020
32020
GIP receptor reduces osteoclast activity and improves osteoblast survival by activating multiple signaling pathways
MS Hansen, K Søe, LL Christensen, P Fernandez-Guerra, NW Hansen, ...
bioRxiv, 2022.07. 02.498420, 2022
22022
Targeting nonsense mutations in maple syrup urine disease
P Fernandez-Guerra, B Merinero, A Oyarzabal, LR Desviat, M Ugarte, ...
JOURNAL OF INHERITED METABOLIC DISEASE 33, S176-S176, 2010
22010
Myalgisk encefalomyelitis eller kronisk træthedssyndrom
L Brinth, H Nielsen, K Varming, SE Boonen, AG Ebsen, ...
Ugeskr Læger 181, V08180570, 2019
12019
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