Cystic fibrosis pulmonary guidelines: chronic medications for maintenance of lung health PA Flume, BP O'Sullivan, KA Robinson, CH Goss, PJ Mogayzel Jr, ... American journal of respiratory and critical care medicine 176 (10), 957-969, 2007 | 805 | 2007 |
Autonomous sweat extraction and analysis applied to cystic fibrosis and glucose monitoring using a fully integrated wearable platform S Emaminejad, W Gao, E Wu, ZA Davies, H Yin Yin Nyein, S Challa, ... Proceedings of the National Academy of sciences 114 (18), 4625-4630, 2017 | 694 | 2017 |
Repeated adeno-associated virus serotype 2 aerosol-mediated cystic fibrosis transmembrane regulator gene transfer to the lungs of patients with cystic fibrosis: a multicenter … RB Moss, D Rodman, LT Spencer, ML Aitken, PL Zeitlin, D Waltz, C Milla, ... Chest 125 (2), 509-521, 2004 | 479 | 2004 |
Trends in pulmonary function in patients with cystic fibrosis correlate with the degree of glucose intolerance at baseline CE Milla, WJ Warwick, A Moran American journal of respiratory and critical care medicine 162 (3), 891-895, 2000 | 419 | 2000 |
Diagnosis, monitoring, and treatment of primary ciliary dyskinesia: PCD foundation consensus recommendations based on state of the art review AJ Shapiro, MA Zariwala, T Ferkol, SD Davis, SD Sagel, SD Dell, ... Pediatric pulmonology 51 (2), 115-132, 2016 | 388 | 2016 |
Diagnosis of primary ciliary dyskinesia. An official American Thoracic Society clinical practice guideline AJ Shapiro, SD Davis, D Polineni, M Manion, M Rosenfeld, SD Dell, ... American journal of respiratory and critical care medicine 197 (12), e24-e39, 2018 | 338 | 2018 |
Repeated aerosolized AAV-CFTR for treatment of cystic fibrosis: a randomized placebo-controlled phase 2B trial RB Moss, C Milla, J Colombo, F Accurso, PL Zeitlin, JP Clancy, ... Human gene therapy 18 (8), 726-732, 2007 | 325 | 2007 |
Cystic fibrosis pulmonary guidelines: pulmonary complications: hemoptysis and pneumothorax PA Flume, PJ Mogayzel Jr, KA Robinson, RL Rosenblatt, L Quittell, ... American journal of respiratory and critical care medicine 182 (3), 298-306, 2010 | 323 | 2010 |
Efficacy and safety of lumacaftor and ivacaftor in patients aged 6–11 years with cystic fibrosis homozygous for F508del-CFTR: a randomised, placebo-controlled phase 3 trial F Ratjen, C Hug, G Marigowda, S Tian, X Huang, S Stanojevic, CE Milla, ... The lancet Respiratory medicine 5 (7), 557-567, 2017 | 320 | 2017 |
Standardizing nasal nitric oxide measurement as a test for primary ciliary dyskinesia MW Leigh, MJ Hazucha, KK Chawla, BR Baker, AJ Shapiro, DE Brown, ... Annals of the American Thoracic Society 10 (6), 574-581, 2013 | 282 | 2013 |
Clinical features of childhood primary ciliary dyskinesia by genotype and ultrastructural phenotype SD Davis, TW Ferkol, M Rosenfeld, HS Lee, SD Dell, SD Sagel, C Milla, ... American journal of respiratory and critical care medicine 191 (3), 316-324, 2015 | 267 | 2015 |
Assessment of clinical response to ivacaftor with lung clearance index in cystic fibrosis patients with a G551D-CFTR mutation and preserved spirometry: a randomised controlled … J Davies, H Sheridan, N Bell, S Cunningham, SD Davis, JS Elborn, ... The lancet Respiratory medicine 1 (8), 630-638, 2013 | 263 | 2013 |
Diabetes is associated with dramatically decreased survival in female but not male subjects with cystic fibrosis CE Milla, J Billings, A Moran Diabetes care 28 (9), 2141-2144, 2005 | 241 | 2005 |
Ivacaftor treatment of cystic fibrosis in children aged 12 to< 24 months and with a CFTR gating mutation (ARRIVAL): a phase 3 single-arm study M Rosenfeld, CE Wainwright, M Higgins, LT Wang, C McKee, D Campbell, ... The lancet respiratory medicine 6 (7), 545-553, 2018 | 237 | 2018 |
Laterality defects other than situs inversus totalis in primary ciliary dyskinesia: insights into situs ambiguus and heterotaxy AJ Shapiro, SD Davis, T Ferkol, SD Dell, M Rosenfeld, KN Olivier, ... Chest 146 (5), 1176-1186, 2014 | 235 | 2014 |
Zebrafish ciliopathy screen plus human mutational analysis identifies C21orf59 and CCDC65 defects as causing primary ciliary dyskinesia C Austin-Tse, J Halbritter, MA Zariwala, RM Gilberti, HY Gee, N Hellman, ... The American Journal of Human Genetics 93 (4), 672-686, 2013 | 231 | 2013 |
Longitudinal changes in growth parameters are correlated with changes in pulmonary function in children with cystic fibrosis ML Peterson, DR Jacobs Jr, CE Milla Pediatrics 112 (3), 588-592, 2003 | 226 | 2003 |
Mutations in RSPH1 Cause Primary Ciliary Dyskinesia with a Unique Clinical and Ciliary Phenotype MR Knowles, LE Ostrowski, MW Leigh, PR Sears, SD Davis, WE Wolf, ... American journal of respiratory and critical care medicine 189 (6), 707-717, 2014 | 223 | 2014 |
Microvascular complications in cystic fibrosis–related diabetes SJ Schwarzenberg, W Thomas, TW Olsen, T Grover, D Walk, C Milla, ... Diabetes care 30 (5), 1056-1061, 2007 | 220 | 2007 |
Risk of death in cystic fibrosis patients with severely compromised lung function CE Milla, WJ Warwick Chest 113 (5), 1230-1234, 1998 | 218 | 1998 |