Resection of hepatocellular adenoma in patients with glycogen storage disease type Ia
SK Reddy, PS Kishnani, JA Sullivan, DD Koeberl… - Journal of …, 2007 - Elsevier
BACKGROUND/AIMS: Because dietary modifications have prolonged the life expectancy of
patients with glycogen storage disease type Ia (GSD Ia), the incidence of hepatocellular
adenoma (HCA) to carcinoma (HCC) transformation is increasing. The objective of this
retrospective study is to assess the safety and effectiveness of HCA resection in GSD Ia
patients. METHODS: Clinicopathologic, peri-operative, and long-term data were reviewed
from patients who underwent HCA resection. Comparisons were made with Fisher's exact …
patients with glycogen storage disease type Ia (GSD Ia), the incidence of hepatocellular
adenoma (HCA) to carcinoma (HCC) transformation is increasing. The objective of this
retrospective study is to assess the safety and effectiveness of HCA resection in GSD Ia
patients. METHODS: Clinicopathologic, peri-operative, and long-term data were reviewed
from patients who underwent HCA resection. Comparisons were made with Fisher's exact …
